Profiles and Development of Adaptive Behavior in Adolescents and Adults with Williams Syndrome

Abstract

Williams Syndrome (WS) is associated with deficits in adaptive behavior and an uneven adaptive profile. This study cross-sectionally examined the profiles and developmental trajectories of adaptive behavior in 100 adolescents and adults with Williams Syndrome ages 12 to 53 years using the Scales o Independent Behavior-Revised (SIB-R). Profile findings indicated a significant weakness in motor skills and community living skills relative to social interaction and communication skills and personal living skills. Age-related decline in Social Interaction and Communication domain was also found in this population. Interventions should address promoting adaptive motor functioning and community living skills while taking their developmental needs into consideration.